Dietary intakes and quality of Irish adults with cystic fibrosis: Comparisons to nutrition guidelines and HEI-2020

dc.contributor.authorGreaney, Cianen
dc.contributor.authorMcCarthy, Ellenen
dc.contributor.authorO'Brien, Laurenen
dc.contributor.authorTecklenborg, Sarahen
dc.contributor.authorHowlett, Ciaraen
dc.contributor.authorCronin, Karenen
dc.contributor.authorLanders, Clodaghen
dc.contributor.authorConnolly, Maryen
dc.contributor.authorO'Sullivan, Derbhlaen
dc.contributor.authorWhiston, Aoifeen
dc.contributor.authorRobinson, Katieen
dc.contributor.authorTierney, Audreyen
dc.contributor.funderHealth Research Boarden
dc.contributor.funderHealth Research Charities Irelanden
dc.contributor.funderCystic Fibrosis Irelanden
dc.date.accessioned2025-07-22T10:59:35Z
dc.date.available2025-07-22T10:59:35Z
dc.date.issued2025 -07-11en
dc.description.abstractBackground: With evolving Cystic Fibrosis (CF) phenotypes resulting from changes to clinical management, healthier dietary practices are warranted for many people with CF. Whilst diet composition is reported, diet quality data is lacking in CF. This study aims to evaluate dietary intakes and diet quality in adults with CF via guideline comparison and a validated diet quality index. Methods: Cross-sectional study of Irish adults with CF. Demographic questionnaires and three-day food diaries were completed. Healthy Eating Index – 2020 (HEI-2020) assessed diet quality. Data was statistically analysed in SPSS®. Results: Of n = 68 participants (female: 58.8 %, age: 35.2 ± 10.1 years, FEV1%: 77.4 ± 25.1 %), 36.8 % were overweight/obese and 77.6 % pancreatic insufficient. While median (interquartile range) percentage estimated average requirement (EAR) was 110.1 (45.3) %, 50.0 % of participants were below CF energy requirements (110 % EAR). Mean percentage total energy intake (%TEI) protein (18.0 ± 3.9 %) aligned to dietary reference values (DRV). %TEI carbohydrates (44.1 ± 6.5 %) was below, and %TEI fat (37.1 ± 5.4 %), saturated fat (14.1 ± 3.3 %) and sugar (17.4 ± 5.6 %) exceeded DRV. Median vitamin A intake was adequate [936.6 (1005.2) µg], but vitamin D [3.6 (4.3) µg], E (9.6 ± 5.2 mg) and K1 [31.1 (71.2) µg] intakes were insufficient without supplementation. Regarding Irish healthy eating guidelines, 95.6 % of participants overconsumed energy-dense nutrient poor (EDNP) foods, with 76.5 % below vegetables, salad and fruit intake guidelines. Participants’ mean HEI-2020 score (0–100) was 59.3 ± 12.4. Conclusion: Findings indicate suboptimal diet quality. Despite reliance on EDNP foods, many did not achieve energy targets. Moving forward, emphasis on diet quality is of paramount importance to improve overall health in people with CF.en
dc.description.sponsorshipHealth Research Charities Ireland / Health Research Board (Joint Funding Scheme 2020 with Cystic Fibrosis Ireland 9HRCI-HRB-2020\u2013025); Irish Research Council (GOIPG/2023/4258)en
dc.description.statusPeer revieweden
dc.description.versionPublished Versionen
dc.format.mimetypeapplication/pdfen
dc.identifier.citationGreaney, C., McCarthy, E., O'Brien, L., Tecklenborg, S., Howlett, C., Cronin, K., Landers, C., Connolly, M., O'Sullivan, D., Whiston, A. and Robinson, K. (2025) 'Dietary intakes and quality of Irish adults with cystic fibrosis: Comparisons to nutrition guidelines and HEI-2020', Journal of Cystic Fibrosis. https://doi.org/10.1016/j.jcf.2025.07.004en
dc.identifier.doi10.1016/j.jcf.2025.07.004en
dc.identifier.issn15691993en
dc.identifier.journaltitleJournal of Cystic Fibrosisen
dc.identifier.urihttps://hdl.handle.net/10468/17736
dc.language.isoenen
dc.publisherElsevier B.V.en
dc.rights© 2025, the Author(s). Published by Elsevier B.V. on behalf of European Cystic Fibrosis Society. This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/)en
dc.rights.urihttps://creativecommons.org/licenses/by/4.0/
dc.subjectCystic fibrosisen
dc.subjectDiet qualityen
dc.subjectFood servesen
dc.subjectMacronutrientsen
dc.subjectMicronutrientsen
dc.titleDietary intakes and quality of Irish adults with cystic fibrosis: Comparisons to nutrition guidelines and HEI-2020en
dc.typeArticle (peer reviewed)en
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